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Hexosaminidase
Hexosaminidase
Overview
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Hydrolase
(19)
NEU4
NEU3
Alpha-N-ac- etylglucosaminidase
Viral neuraminidase
Iduronidase
Iduronidase
NEU2
Fucosidase
Alpha-mannosidase
Alpha-glucosidase
Hyaluronidase
Lysozyme
Maltase-gl- ucoamylase
NEU1
Neuraminidase
Galactosyl- ceramidase
Arylsulfatase A
Sucrase
Glucocerebrosidase
Maltase
more...
Hydrolases
(11)
Beta galactosidase
Alpha-N-ac- etylglucosaminidase
Iduronidase
Fucosidase
Alpha-mannosidase
Alpha-mannosidase
Alpha-glucosidase
Galactosyl- ceramidase
Arylsulfatase A
Sucrase
Glucocerebrosidase
Maltase
more...
EC numbers (EC 3)
(10)
Alpha-N-ac- etylglucosaminidase
Iduronidase
Fucosidase
Alpha-mannosidase
Alpha-glucosidase
Alpha-glucosidase
Galactosyl- ceramidase
Arylsulfatase A
Sucrase
Glucocerebrosidase
Maltase
more...
Enzyme
(16)
Dolichol kinase
Glycogen debranching enzyme
Galactosidases
Disaccharidase
Pullulanase
Pullulanase
Enzyme activator
Alpha-N-ac- etylglucosaminidase
Iduronidase
Fucosidase
Alpha-mannosidase
Alpha-glucosidase
Galactosyl- ceramidase
Arylsulfatase A
Sucrase
Glucocerebrosidase
Maltase
more...
EC number
(11)
Alpha-N-ac- etylglucosaminidase
Iduronidase
Fucosidase
Alpha-mannosidase
Alpha-glucosidase
Alpha-glucosidase
Glycogen debranching enzyme
Galactosyl- ceramidase
Arylsulfatase A
Sucrase
Glucocerebrosidase
Maltase
more...
Enzymes
(13)
Alpha-N-ac- etylgalactosaminidase
Dna glycosylases
Amylase
Alpha-amylase
Enzyme
Enzyme
Fucosidase
Dolichol kinase
Alpha-glucosidase
Galactosidases
Disaccharidase
Beta galactosidase
Pullulanase
Enzyme activator
more...
EC 3.2.1
(67)
Bacterial neuraminidase
Glucuronidase
Invertase
Trehalase
1,2-alpha-- L-fucosidase
1,2-alpha-- L-fucosidase
1,3-alpha-- L-fucosidase
1,6-alpha-- D-mannosidase
1,6-alpha-- L-fucosidase
2-deoxyglucosidase
3-deoxyoctulosonase
3alpha(S)-- strictosidine beta-glucosidase
6-phospho-- beta-galactosidase
6-phospho-- beta-glucosidase
Alpha,alph- a-phosphotrehalase
Alpha,alph- a-trehalase
Alpha-L-fucosidase
Alpha-N-ac- etylgalactosaminidase
Alpha-amylase
Alpha-glucosidase
Alpha-glucuronidase
Amygdalin beta-glucosidase
Amylase
Beta galactosidase
Beta-L-ara- binosidase
Beta-apios- yl-beta-glucosidase
Beta-glucosidase
Beta-prime- verosidase
Chitinase
Coniferin beta-glucosidase
Cyclomalto- dextrinase
Difructose- -anhydride synthase
Dispersin B
Endoglycos- ylceramidase
GDP-glucosidase
GH family
Galactosyl- ceramidase
Galactosyl- galactosylglucosylceramidase
Galacturan 1,4-alpha-- galacturonidase
Glucocerebrosidase
Glucosylceramidase
Glucuronos- yl-disulfoglucosamine glucuronidase
Glycoside hydrolase
Glycoside hydrolase family 1
Glycosylceramidase
Glycyrrhizinate beta-glucuronidase
Hyaluronidase
Klotho (biology)
Lactase
Linamarase
Lysozyme
Maltase
Maltose-6'- -phosphate glucosidase
Mucinaminylserine mucinaminidase
Neuraminidase
Protein-gl- ucosylgalactosylhydroxylysine glucosidase
Prunasin beta-glucosidase
Quercitrinase
Raucaffricine beta-glucosidase
Sacrosidase
Steryl-bet- a-glucosidase
Sucrase
Thioglucosidase
Vicianin beta-glucosidase
Viral neuraminidase
Xylanase
Xyloglucan-specific endo-beta-- 1,4-glucanase
Xyloglucan-specific exo-beta-1- ,4-glucanase
more...
Lipid storage disorders
(14)
GM2 gangliosidosis
Gangliosidosis
Gaucher disease
Niemann Pick disease
Sandhoff disease
Sandhoff disease
Tay Sachs disease
Fabry disease
Farber disease
GM1 gangliosidoses
Krabbe disease
Multiple sulfatase deficiency
Niemann-Pick disease, type C
Schindler disease
Wolman disease
more...
Lysosomal storage diseases
(40)
Lipid storage disorder
Lysosomal storage disease
Alpha-mannosidosis
Aspartylgl- ucosaminuria
Batten disease
Batten disease
Canavan disease
Cholesteryl ester storage disease
Cystinosis
Fabry disease
Farber disease
GM1 gangliosidoses
GM2 gangliosidosis
Galactosialidosis
Gangliosidosis
Gaucher disease
Glycogen storage disease type II
Glycoproteinosis
Hunter syndrome
Hurler syndrome
I-cell disease
Krabbe disease
Metachromatic leukodystrophy
Morquio syndrome
Mucolipidosis
Mucolipidosis type IV
Mucopolysa- ccharidosis
Multiple sulfatase deficiency
Neuronal ceroid lipofuscinosis
Niemann Pick disease
Niemann-Pick disease, type C
Pseudo-Hurler polydystrophy
Pycnodysostosis
Salla disease
Sandhoff disease
Sanfilippo syndrome
Schindler disease
Sialidosis
Sly syndrome
Tay Sachs disease
Wolman disease
more...
Metabolic disorders
(60)
Activated protein C resistance
Adenosine deaminase deficiency
Albinism
Alcohol flush reaction
Antithrombin III deficiency
Antithrombin III deficiency
Baker IDI Heart and Diabetes Institute
Blue diaper syndrome
Childhood obesity
Congenital disorder of glycosylation
Congenital hyperinsulinism
Crigler-Najjar syndrome
Diagnostic fast
Disaccharidase
Disorders of calcium metabolism
Ectopic calcification
Farber disease
Fructose malabsorption
GM1 gangliosidoses
GM2 gangliosidosis
Galactosemia
Galactosemic cataract
Gangliosidosis
Gaucher disease
Glycogen storage disease type 0
Hereditary fructose intolerance
Homocystinuria
Hyperglycemia
Hyperinsulinemic hypoglycemia
Hyperinsulinism
Hypoglycemia
Inborn errors of metabolism
Ketotic hypoglycemia
Krabbe disease
Lactose intolerance
Lipid storage disorders
List of causes of hypoglycemia
Metab-L
Methemoglobinemia
Neuronal ceroid lipofuscinosis
Niemann Pick disease
Niemann-Pick disease, type C
Obesity
Obesogen
Pickardt syndrome
Pycnodysostosis
Refeeding syndrome
Richner Hanhart syndrome
Rotor syndrome
Salicylate sensitivity
Schindler disease
Selfish Brain Theory
Sitosterolemia
Stress hyperglycemia
Sucrose intolerance
Tay Sachs disease
Triosephosphate isomerase deficiency
Urbach–Wiethe disease
Urea cycle disorder
Winchester syndrome
Wolman disease
more...
Ashkenazi Jews topics
Ashkenazi Jewish
Bloom syndrome
GM2 gangliosidosis
Tay Sachs disease
Niemann Pick disease
Gaucher disease
Lipids
Gangliosides
Globosides
Glycolipid
GM1
Gene
(12)
HEXB
Sphingomyelin phosphodiesterase 1
ACER3
ACER2
ASAH1
ASAH1
ACER1
GM2A
ASAH2
NEU4
NEU3
NEU2
Fucosidase
more...
See also
(20)
GM2 (ganglioside)
SLC17A5
Hexosamine
GM2-gangliosidosis, AB variant
Genetic disorders
Genetic disorders
Hexokinase
Hexa
Startle reaction
Hexoses
Autosomal recessive
Oligosaccharides
Anatomy
Lysosomal
Beta-D
HEXA
Manba (disambiguation)
NAGA (gene)
Inherited disorder
Sphingolipidoses
Iodine deficiency
more...
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